Отчеты о заболеваниях полости рта

Papillon-Lefevre Syndrome in 9 Year Old Peadatric Patient: A Rare Case Presentation with Comprehensive Review

Abstract

Manjul Tiwari

Papillon-Lefevre syndrome is a rare autosomal recessive disorder in which the frequently observed manifestations are palm plantar keratinization and premature loss of both deciduous and permanent teeth. Here I present a rare case report of Papillon-Lefevre syndrome in 9 year old Peadatric patient along with a comprehensive review of the etiology, pathology, clinical features, differential diagnosis and management of the condition.