Журнал клинических случаев

Pleomorphic Rhabdomyosarcoma with Neuroendocrine Differentiation in Abdominal Wall

Abstract

Faviana P, Bartolucci A, Boldrini L, Musco B, Farci F, Ferrari M, Ricci A and Lippolis P

The present study presents a case of primary pleomorphic rhabdomyosarcoma that occurs in the abdominal wall. A 52-year-old patient arrived in our department. In his clinical history they have been: 2016 advanced serous ovary papillary carcinoma; a diagnosis of a primary gynecological tumor with secondary extension, and the patient was prepared for bilateral total abdominal hysterectomy salpingo-oophorectomy, omentectomy. Macroscopic and histopathological evaluation of the specimen removed surgically showed a medially differentiated serous papillary carcinoma. The patient received Carbo-Taxol and avastin as postoperative chemotherapy. Postoperative followup and CT twelve months after surgery, revealed signs of tumor recurrence: two multilobate neoformations of 15 cm and 5 cm in size respectively with intestinal obstruction. The final histological diagnosis was pleomorphic rhabdomyosarcoma with neuroendocrine differentiation.