Журнал клинических случаев

Primary Primitive Neuroectodermal Tumor of the Urinary Bladder: A Case Report of a Rare Pathological Entity with a Rapidly Progressing Clinical Course

Abstract

Klein Ilan, Freifeld Yuval and Dekel Yoram

Primary primitive neuroectodermal tumors (PNET) are a group of malignant neoplasms composed of sheets of uniform small round cells that exhibit neuroblastic differentiation outside the nervous system. They are closely related to Ewing’s sarcoma and predominantly affect children and adolescents. There are few reports of primary visceral PNET’s in the literature, most of them in the urogential organs, and even fewer reports of PNET’s of the urinary bladder. Thus, every case counts in increasing the pool of knowledge as far as the symptoms, risk factors, histopathology and treatment of this rare and aggressive entity. We present such a case.