Журнал клинических случаев

The Ultimate Stage of Rasmussen ’ s Encephalitis

Abstract

Younes Samia, Daoussi Nizar, Mokni Narjes, Boughammoura Amel, Aissi Mouna, Frih-Ayed Mahbouba, Jerbi Saida and Sfar Mohamed Habib

Rasmussen encephalitis (RE) is a rare and progressive disease of childhood. We report the case of 14-year-old girl who presented with recurrent partial and generalized epileptic seizures with mental impairment and progressive left sided hemiplegia. EEG showed slowing of the background activity and paroxysmal discharges of slow waves in the right hemisphere. Serial MRI brain scans revealed an important atrophy of the right hemisphere with dilatation of the ipsilateral lateral ventricle. The residual phase, characterized by decrease in seizure frequency and stabilization in the hemiparesis, constitute the ultimate stage of RE.